RTL9

Chr X

retrotransposon Gag like 9

Also known as: MAR9, MART9, RGAG1, SIRH10

RTL9 encodes a retrotransposon-like protein involved in transcriptional regulation and chromatin organization. Mutations cause autosomal recessive developmental delay with seizures, intellectual disability, and growth retardation, typically presenting in infancy or early childhood. The gene is highly constrained against loss-of-function variants, indicating that complete loss of RTL9 function is poorly tolerated.

LOEUF 0.22
Clinical SummaryRTL9
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.22LOEUF
pLI 0.997
Z-score 4.13
OE 0.05 (0.010.22)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
-0.67Z-score
OE missense 1.08 (1.011.16)
568 obs / 524.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.05 (0.010.22)
00.351.4
Missense OE1.08 (1.011.16)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 1 / 21.8Missense obs/exp: 568 / 524.9Syn Z: -0.29

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RTL9 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found