RRN3

Chr 16

RNA polymerase I transcription factor RRN3

Also known as: A-270G1.2, TIFIA

The RRN3 protein is required for efficient transcription initiation by RNA polymerase I and formation of the competent pre-initiation complex in the nucleolus. Mutations cause autosomal recessive developmental delays, intellectual disability, and growth retardation with onset in infancy or early childhood. This gene is highly constrained against loss-of-function variants in the general population.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.65
Clinical SummaryRRN3
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.65LOEUF
pLI 0.000
Z-score 3.15
OE 0.41 (0.270.65)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.77Z-score
OE missense 1.12 (1.031.22)
381 obs / 341.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.41 (0.270.65)
00.351.4
Missense OE1.12 (1.031.22)
00.61.4
Synonymous OE1.26
01.21.6
LoF obs/exp: 14 / 33.8Missense obs/exp: 381 / 341.0Syn Z: -2.32

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RRN3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗