RPS8

Chr 1

ribosomal protein S8

The RPS8 protein is a component of the small 40S ribosomal subunit and participates in ribosome assembly in the nucleolus, where it helps generate the ribonucleoprotein complexes responsible for protein synthesis. Mutations in this highly constrained gene (pLI 0.99) cause neurodevelopmental disorders with developmental delay, intellectual disability, and growth retardation, following an autosomal dominant inheritance pattern. Clinical features typically manifest in early childhood and may include microcephaly and other growth-related abnormalities.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.22
Clinical SummaryRPS8
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.99). One damaged copy is likely sufficient to cause disease.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.22LOEUF
pLI 0.990
Z-score 3.45
OE 0.00 (0.000.22)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.42Z-score
OE missense 0.40 (0.310.50)
50 obs / 126.5 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.00 (0.000.22)
00.351.4
Missense OE0.40 (0.310.50)
00.61.4
Synonymous OE1.10
01.21.6
LoF obs/exp: 0 / 13.8Missense obs/exp: 50 / 126.5Syn Z: -0.56
DN
0.17100th %ile
GOF
0.07100th %ile
LOF
0.86top 5%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.22

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RPS8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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