RPS4Y1

Chr Y

ribosomal protein S4 Y-linked 1

Also known as: RPS4Y, S4

This gene encodes ribosomal protein S4, a component of the 40S ribosomal subunit that catalyzes protein synthesis in the cytoplasm. Located on the Y chromosome, RPS4Y1 has a functionally equivalent X-linked counterpart (RPS4X), and haploinsufficiency of ribosomal protein S4 genes has been suggested to contribute to Turner syndrome, though this remains controversial. The gene shows moderate constraint against loss-of-function variants (pLI 0.63, LOEUF 0.94).

OMIMResearchSummary from RefSeq
LOFmechanismLOEUF 0.94
Clinical SummaryRPS4Y1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.63) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
61 unique Pathogenic / Likely Pathogenic· 6 VUS of 104 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.94LOEUF
pLI 0.627
Z-score 1.64
OE 0.00 (0.000.94)
Moderately constrained

Typical tolerance to LoF variation

Missense Constraint
1.12Z-score
OE missense 0.54 (0.400.76)
26 obs / 47.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.94)
00.351.4
Missense OE0.54 (0.400.76)
00.61.4
Synonymous OE1.28
01.21.6
LoF obs/exp: 0 / 3.1Missense obs/exp: 26 / 47.8Syn Z: -0.86
DN
0.4884th %ile
GOF
0.2597th %ile
LOF
0.65top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

104 submitted variants in ClinVar

Classification Summary

Pathogenic59
Likely Pathogenic2
VUS6
59
Pathogenic
2
Likely Pathogenic
6
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
59
Likely Pathogenic
2
VUS
6
Likely Benign
0
Benign
0
Total67

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RPS4Y1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →