The protein is predicted to be located in cellular membranes, but its specific molecular function remains unknown. No established disease associations or inheritance patterns have been reported for RPRML mutations. The predicted gain-of-function mechanism suggests that pathogenic variants may result in increased or abnormal protein activity.

Summary from RefSeq, Mechanism
0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.51
LOEUF
GOF
Mechanism· predicted
Clinical SummaryRPRML
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.00) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.51LOEUF
pLI 0.464
Z-score 1.18
OE 0.00 (0.001.51)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.40Z-score
OE missense 0.85 (0.671.08)
48 obs / 56.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.001.51)
00.351.4
Missense OE0.85 (0.671.08)
00.61.4
Synonymous OE0.81
01.21.6
LoF obs/exp: 0 / 1.6Missense obs/exp: 48 / 56.4Syn Z: 0.78
DN
0.5082th %ile
GOF
0.86top 5%
LOF
0.4332th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RPRML · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →