RPL19

Chr 17

ribosomal protein L19

Also known as: L19, eL19

The protein is a component of the large 60S ribosomal subunit that synthesizes proteins in the cell. Mutations cause autosomal dominant ribosomopathy through loss of function, leading to impaired protein synthesis. The high constraint scores (pLI 0.98, LOEUF 0.24) indicate this gene is highly intolerant to loss-of-function variants.

Summary from RefSeq, UniProt, Mechanism
0
Active trials
18
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.24
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryRPL19
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.98). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.24LOEUF
pLI 0.982
Z-score 3.24
OE 0.00 (0.000.24)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.39Z-score
OE missense 0.42 (0.340.53)
58 obs / 136.6 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.00 (0.000.24)
00.351.4
Missense OE0.42 (0.340.53)
00.61.4
Synonymous OE1.12
01.21.6
LoF obs/exp: 0 / 12.2Missense obs/exp: 58 / 136.6Syn Z: -0.61
DN
0.3296th %ile
GOF
0.14100th %ile
LOF
0.82top 5%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.24

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RPL19 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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