RNU12

Chr 22AR

RNA, U12 small nuclear

RNU12 encodes the U12 small nuclear RNA component of the U12 snRNP complex, which is essential for splicing of U12-type introns in pre-mRNA processing. Mutations cause autosomal recessive spinocerebellar ataxia 33 and CDAGS syndrome (craniosynostosis, delayed closure of fontanelles, cranial defects, clavicular hypoplasia, anal defects, and skin eruption). Both conditions follow autosomal recessive inheritance and involve neurological dysfunction along with additional developmental abnormalities in CDAGS syndrome.

OMIMResearchSummary from RefSeq, OMIM
AR2 OMIM phenotypes
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Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RNU12 · protein map & ClinVar variants

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3D Protein StructureAlphaFold

Clinical Trials

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