RMP24

Chr 18

ribonuclease MRP subunit p24

Also known as: C18orf21, HsT3108, PNAS-124, PNAS-131, XTP13

RMP24 encodes a specific component of the MRP ribonucleoprotein endoribonuclease complex that processes pre-ribosomal RNA. Mutations cause cartilage-hair hypoplasia, an autosomal recessive disorder characterized by short-limbed dwarfism, fine sparse hair, and immunodeficiency. The condition typically presents in infancy with growth retardation and recurrent infections due to T-cell dysfunction.

Summary from UniProt
Research Assistant →
0
Active trials
3
Pubs (1 yr)
43
P/LP submissions
P/LP missense
LOEUF
Mechanism
Clinical SummaryRMP24
📋
ClinVar Variants
41 unique Pathogenic / Likely Pathogenic of 42 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/RMP24?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

42 submitted variants in ClinVar

Classification Summary

Pathogenic39
Likely Pathogenic2
Likely Benign1
39
Pathogenic
2
Likely Pathogenic
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
39
Likely Pathogenic
2
VUS
0
Likely Benign
1
Benign
0
Total42

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RMP24 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 2 full-text resultsSearch PubTator3 ↗
Key Publications
Landmark & review papers · by relevance
PubMed
Top 3 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found