RLN3

Chr 19

relaxin 3

Also known as: H3, RXN3, ZINS4, insl7

The RLN3 protein is a neuropeptide hormone that functions as a ligand for receptors LGR7, RXFP3, and RXFP4, regulating stress, memory, and appetite in the brain. Mutations in RLN3 cause neurodevelopmental disorders with intellectual disability and behavioral abnormalities, inherited in an autosomal recessive pattern. The gene shows tolerance to loss-of-function variants (low constraint), suggesting that complete loss of function may be required for disease manifestation.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
3
Pubs (1 yr)
13
P/LP submissions
0%
P/LP missense
1.66
LOEUF
DN
Mechanism· predicted
Clinical SummaryRLN3
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
13 unique Pathogenic / Likely Pathogenic· 25 VUS of 44 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.66LOEUF
pLI 0.013
Z-score 0.57
OE 0.70 (0.321.66)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.16Z-score
OE missense 1.05 (0.891.24)
95 obs / 90.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.70 (0.321.66)
00.351.4
Missense OE1.05 (0.891.24)
00.61.4
Synonymous OE0.75
01.21.6
LoF obs/exp: 3 / 4.3Missense obs/exp: 95 / 90.7Syn Z: 1.24
DN
0.80top 10%
GOF
0.4382th %ile
LOF
0.2775th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

44 submitted variants in ClinVar

Classification Summary

Pathogenic12
Likely Pathogenic1
VUS25
Likely Benign4
Conflicting2
12
Pathogenic
1
Likely Pathogenic
25
VUS
4
Likely Benign
2
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
12
0
12
Likely Pathogenic
0
0
1
0
1
VUS
0
21
4
0
25
Likely Benign
0
2
2
0
4
Benign
0
0
0
0
0
Conflicting
2
Total02319044

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RLN3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗