RGS17

Chr 6

regulator of G protein signaling 17

Also known as: RGS-17, RGSZ2, hRGS17

This protein regulates G-protein coupled receptor signaling by accelerating GTPase activity of specific G alpha subunits (GNAZ and GNAI2), thereby terminating signals from receptors including muscarinic acetylcholine and dopamine receptors. Mutations in RGS17 have not been definitively associated with human disease. The gene shows moderate tolerance to loss-of-function variants (LOEUF 0.641), suggesting haploinsufficiency may not be highly pathogenic.

ResearchSummary from RefSeq, UniProt
LOEUF 0.64
Clinical SummaryRGS17
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.25) despite low pLI — interpret in context.
📋
ClinVar Variants
23 unique Pathogenic / Likely Pathogenic· 20 VUS of 45 total submissions
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.64LOEUF
pLI 0.267
Z-score 2.42
OE 0.25 (0.110.64)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.94Z-score
OE missense 0.74 (0.620.90)
79 obs / 106.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.25 (0.110.64)
00.351.4
Missense OE0.74 (0.620.90)
00.61.4
Synonymous OE0.86
01.21.6
LoF obs/exp: 3 / 12.1Missense obs/exp: 79 / 106.2Syn Z: 0.63

ClinVar Variant Classifications

45 submitted variants in ClinVar

Classification Summary

Pathogenic22
Likely Pathogenic1
VUS20
22
Pathogenic
1
Likely Pathogenic
20
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
22
0
22
Likely Pathogenic
0
0
1
0
1
VUS
0
17
3
0
20
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total01726043

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RGS17 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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