RECQL

Chr 12

RecQ like helicase

Also known as: RECON, RECQL1, RecQ1

The protein encoded by this gene is a member of the RecQ DNA helicase family. DNA helicases are enzymes involved in various types of DNA repair, including mismatch repair, nucleotide excision repair and direct repair. The encoded protein is involved in the processing of Holliday junctions, the suppression of sister chromatid exchanges, telomere maintenance, and is required for genotoxic stress resistance. Defects in this gene have been associated with several types of cancer. [provided by RefSeq, Jan 2017]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtRECON progeroid syndrome

Clinical highlights

Gene-disease validity (ClinGen)
hereditary breast carcinoma · ADDisputedevidence questions this relationship2 gene-disease associations curated in total
0
Active trials
12
Pubs (1 yr)
P/LP submissions
P/LP missense
1.31
LOEUF
DN
Mechanism· predicted
📖
GeneReview available — RECQL
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.31LOEUF
pLI 0.000
Z-score 0.16
OE 0.97 (0.731.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.25Z-score
OE missense 0.96 (0.881.05)
322 obs / 334.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.97 (0.731.31)
00.351.4
Missense OE?0.96 (0.881.05)
00.61.4
Synonymous OE?1.04
01.21.6
LoF obs/exp: 31 / 32.0Missense obs/exp: 322 / 334.8Syn Z: -0.38

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RECQL · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →