RBMY1E

Chr Y

RNA binding motif protein Y-linked family 1 member E

The protein is an RNA-binding protein that participates in pre-mRNA splicing during spermatogenesis and is required for normal sperm development. Mutations cause male infertility due to azoospermia or severe oligospermia, inherited in a Y-linked pattern since the gene is located on chromosome Y. The gene has multiple functional copies in the AZFb region and shows relatively low constraint to loss-of-function variation.

ResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.89
Clinical SummaryRBMY1E
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.00) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.89LOEUF
pLI 0.291
Z-score 0.29
OE 0.00 (0.001.89)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.49Z-score
OE missense 1.67 (0.851.95)
7 obs / 4.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.00 (0.001.89)
00.351.4
Missense OE1.67 (0.851.95)
00.61.4
Synonymous OE2.53
01.21.6
LoF obs/exp: 0 / 0.1Missense obs/exp: 7 / 4.2Syn Z: -1.51
DN
0.7326th %ile
GOF
0.4184th %ile
LOF
0.4233th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RBMY1E · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found