RBM46

Chr 4

RNA binding motif protein 46

Also known as: CT68

RBM46 encodes an RNA-binding protein essential for male and female fertility that regulates germ cell development by controlling the mitotic-to-meiotic transition and ensuring proper meiosis prophase I progression. Mutations cause infertility disorders affecting reproductive function, with an autosomal recessive inheritance pattern. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.484), indicating some intolerance to complete loss of protein function.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
5
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.48
LOEUF
Mechanism
Clinical SummaryRBM46
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.21) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.48LOEUF
pLI 0.473
Z-score 3.18
OE 0.21 (0.100.48)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.10Z-score
OE missense 0.64 (0.570.73)
178 obs / 276.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.21 (0.100.48)
00.351.4
Missense OE0.64 (0.570.73)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 4 / 18.9Missense obs/exp: 178 / 276.4Syn Z: 0.42

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RBM46 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →