RBM18

Chr 9

RNA binding motif protein 18

The protein encoded by this gene binds RNA and is found in the cytosol, nucleoplasm, and intercellular bridges during cell division. This gene is highly constrained against loss-of-function variants (pLI = 0.0004), suggesting that mutations would likely cause severe disease, though specific associated disorders have not yet been established in the literature.

ResearchSummary from RefSeq
DNmechanismLOEUF 1.10
Clinical SummaryRBM18
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
28 unique Pathogenic / Likely Pathogenic· 20 VUS of 57 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.10LOEUF
pLI 0.000
Z-score 1.32
OE 0.59 (0.331.10)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.48Z-score
OE missense 0.86 (0.721.03)
85 obs / 98.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.59 (0.331.10)
00.351.4
Missense OE0.86 (0.721.03)
00.61.4
Synonymous OE0.91
01.21.6
LoF obs/exp: 7 / 11.9Missense obs/exp: 85 / 98.4Syn Z: 0.41
DN
0.7133th %ile
GOF
0.5759th %ile
LOF
0.4039th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

57 submitted variants in ClinVar

Classification Summary

Pathogenic27
Likely Pathogenic1
VUS20
27
Pathogenic
1
Likely Pathogenic
20
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
27
0
27
Likely Pathogenic
0
0
1
0
1
VUS
0
19
1
0
20
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total01929048

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RBM18 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found