RBM12B

Chr 8

RNA binding motif protein 12B

Also known as: MGC:33837

Enables RNA binding activity. Predicted to be involved in regulation of RNA splicing. Predicted to be part of ribonucleoprotein complex. Predicted to be active in nucleoplasm. [provided by Alliance of Genome Resources, Jul 2025]

0
Active trials
0
Pubs (1 yr)
7
P/LP submissions
0%
P/LP missense
0.54
LOEUF
DN
Mechanism· predicted
Clinical SummaryRBM12B
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.32) despite low pLI — interpret in context.
📋
ClinVar Variants
7 unique Pathogenic / Likely Pathogenic· 87 VUS of 107 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.54LOEUF
pLI 0.005
Z-score 3.55
OE 0.32 (0.200.54)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.86Z-score
OE missense 0.90 (0.830.97)
514 obs / 571.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.32 (0.200.54)
00.351.4
Missense OE0.90 (0.830.97)
00.61.4
Synonymous OE1.19
01.21.6
LoF obs/exp: 10 / 31.5Missense obs/exp: 514 / 571.8Syn Z: -2.14
DN
0.7133th %ile
GOF
0.5562th %ile
LOF
0.3744th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

107 submitted variants in ClinVar

Classification Summary

Pathogenic7
VUS87
Likely Benign9
7
Pathogenic
87
VUS
9
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
7
0
7
Likely Pathogenic
0
0
0
0
0
VUS
0
87
0
0
87
Likely Benign
0
8
0
1
9
Benign
0
0
0
0
0
Total09571103

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RBM12B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found