RAD52

Chr 12

RAD52 DNA repair protein

This protein is essential for DNA double-strand break repair and homologous recombination, binding single-stranded DNA ends and promoting the annealing of complementary DNA strands while stimulating RAD51 recombinase activity. Mutations cause autosomal recessive primary immunodeficiency with microcephaly and growth retardation, affecting immune system development and neurological growth. The gene is highly constrained against loss-of-function variants, indicating that complete loss of RAD52 function is likely incompatible with normal development.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
40
Pubs (1 yr)
65
P/LP submissions
0%
P/LP missense
1.11
LOEUF
Mechanism
Clinical SummaryRAD52
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
65 unique Pathogenic / Likely Pathogenic· 56 VUS of 178 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.11LOEUF
pLI 0.000
Z-score 1.14
OE 0.76 (0.531.11)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.55Z-score
OE missense 0.90 (0.811.01)
222 obs / 246.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.76 (0.531.11)
00.351.4
Missense OE0.90 (0.811.01)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 19 / 25.1Missense obs/exp: 222 / 246.4Syn Z: -0.02

ClinVar Variant Classifications

178 submitted variants in ClinVar

Classification Summary

Pathogenic61
Likely Pathogenic4
VUS56
Likely Benign11
Benign2
61
Pathogenic
4
Likely Pathogenic
56
VUS
11
Likely Benign
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
61
0
61
Likely Pathogenic
0
0
4
0
4
VUS
1
34
21
0
56
Likely Benign
0
3
7
1
11
Benign
0
1
1
0
2
Total138941134

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

RAD52 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗