RAD18

Chr 3

RAD18 E3 ubiquitin protein ligase

Also known as: RNF73

RAD18 encodes an E3 ubiquitin-protein ligase that mono-ubiquitinates PCNA during postreplication repair of UV-damaged DNA, functioning through interaction with the E2 ubiquitin conjugating enzyme UBE2B. Mutations cause a DNA repair disorder characterized by extreme UV sensitivity, growth retardation, and developmental delays, inherited in an autosomal recessive pattern. The gene shows no constraint against loss-of-function variants in the general population.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.99
Clinical SummaryRAD18
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.99LOEUF
pLI 0.000
Z-score 1.60
OE 0.65 (0.440.99)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.14Z-score
OE missense 1.02 (0.931.13)
267 obs / 260.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.65 (0.440.99)
00.351.4
Missense OE1.02 (0.931.13)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 16 / 24.5Missense obs/exp: 267 / 260.8Syn Z: -0.39

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RAD18 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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