PWWP3B

Chr X

PWWP domain containing 3B

Also known as: MUM1L1

This gene encodes a protein containing a mutated melanoma-associated antigen 1 domain that is expressed at high levels in certain cancers. Biallelic mutations in PWWP3B cause a severe neurodevelopmental disorder characterized by intellectual disability, seizures, and distinctive facial features, following an autosomal recessive inheritance pattern. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.531), consistent with its role in normal neurodevelopment.

Summary from RefSeq
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0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.53
LOEUF
Mechanism
Clinical SummaryPWWP3B
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.21) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.53LOEUF
pLI 0.483
Z-score 2.81
OE 0.21 (0.090.53)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.12Z-score
OE missense 0.98 (0.881.09)
217 obs / 221.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.21 (0.090.53)
00.351.4
Missense OE0.98 (0.881.09)
00.61.4
Synonymous OE1.22
01.21.6
LoF obs/exp: 3 / 14.6Missense obs/exp: 217 / 221.9Syn Z: -1.54

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PWWP3B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found