PTPRF

Chr 1AR

protein tyrosine phosphatase receptor type F

Also known as: BNAH2, LAR

The protein functions as a receptor-type protein tyrosine phosphatase that regulates cell-cell contacts at adherens junctions and controls beta-catenin signaling, while also dephosphorylating EPHA2 to regulate its activity. Mutations cause autosomal recessive aplasia or hypoplasia of breasts and/or nipples. This gene is highly constrained against loss-of-function variants (pLI ~1.0, LOEUF 0.187), indicating that complete loss of function is likely incompatible with normal development.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.191 OMIM phenotype
Clinical SummaryPTPRF
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.19LOEUF
pLI 1.000
Z-score 7.86
OE 0.11 (0.070.19)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.80Z-score
OE missense 0.78 (0.740.82)
990 obs / 1270.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.11 (0.070.19)
00.351.4
Missense OE0.78 (0.740.82)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 10 / 90.8Missense obs/exp: 990 / 1270.4Syn Z: -0.60
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedPTPRF-related atheliaLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.4487th %ile
GOF
0.4875th %ile
LOF
0.65top 25%

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PTPRF · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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