PTPN1

Chr 20AD

protein tyrosine phosphatase non-receptor type 1

Also known as: PTP1B

The protein encoded by this gene is the founding member of the protein tyrosine phosphatase (PTP) family, which was isolated and identified based on its enzymatic activity and amino acid sequence. PTPs catalyze the hydrolysis of the phosphate monoesters specifically on tyrosine residues. Members of the PTP family share a highly conserved catalytic motif, which is essential for the catalytic activity. PTPs are known to be signaling molecules that regulate a variety of cellular processes including cell growth, differentiation, mitotic cycle, and oncogenic transformation. This PTP has been shown to act as a negative regulator of insulin signaling by dephosphorylating the phosphotryosine residues of insulin receptor kinase. This PTP was also reported to dephosphorylate epidermal growth factor receptor kinase, as well as JAK2 and TYK2 kinases, which implicated the role of this PTP in cell growth control, and cell response to interferon stimulation. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2013]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

{Insulin resistance, susceptibility to}MIM #125853
AD

Clinical highlights

Interpreting a novel variant
This gene is strongly intolerant of loss-of-function variation in the population, so LoF variants warrant close attention. No curated mechanism annotation is available — see the mechanism card for the computational prediction and its caveats.Based on population constraint only.
0
Active trials
74
Pubs (1 yr)
P/LP submissions
P/LP missense
0.38
LOEUF
Multiple*
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.38LOEUF
pLI 0.813
Z-score 3.98
OE 0.18 (0.090.38)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
2.79Z-score
OE missense 0.51 (0.440.59)
129 obs / 254.2 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.18 (0.090.38)
00.351.4
Missense OE?0.51 (0.440.59)
00.61.4
Synonymous OE?0.95
01.21.6
LoF obs/exp: 5 / 27.5Missense obs/exp: 129 / 254.2Syn Z: 0.41

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PTPN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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