PRC1

Chr 15

protein regulator of cytokinesis 1

Also known as: ASE1, MAP65

This gene encodes a key regulator of cytokinesis that cross-links antiparallel microtubules and is essential for controlling midzone formation and successful cell division. Biallelic mutations cause microcephaly with chorioretinopathy, which involves neurodevelopmental abnormalities and eye malformations with autosomal recessive inheritance. The gene is highly constrained against loss-of-function variants (LOEUF 0.621), reflecting its essential role in cell division.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 0.62
Clinical SummaryPRC1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.62LOEUF
pLI 0.000
Z-score 3.58
OE 0.42 (0.290.62)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.28Z-score
OE missense 0.96 (0.871.05)
332 obs / 346.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.42 (0.290.62)
00.351.4
Missense OE0.96 (0.871.05)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 19 / 44.9Missense obs/exp: 332 / 346.8Syn Z: -0.69
DN
0.6743th %ile
GOF
0.4973th %ile
LOF
0.3162th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PRC1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗