PPP1R7

Chr 2

protein phosphatase 1 regulatory subunit 7

Also known as: SDS22

This gene encodes a regulatory subunit of protein phosphatase 1 that is required for completion of the mitotic cycle and targets the phosphatase to mitotic kinetochores. The gene is highly constrained against loss-of-function variants (pLI 0.99, LOEUF 0.24), but no definitive disease associations have been established in the provided data. Additional clinical and functional studies would be needed to determine if mutations in this gene cause human disease.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
106
P/LP submissions
0%
P/LP missense
0.24
LOEUF· LoF intol.
Mechanism
Clinical SummaryPPP1R7
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.99). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
104 unique Pathogenic / Likely Pathogenic· 55 VUS of 177 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.24LOEUF
pLI 0.995
Z-score 3.93
OE 0.05 (0.020.24)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.86Z-score
OE missense 0.64 (0.560.74)
138 obs / 214.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.05 (0.020.24)
00.351.4
Missense OE0.64 (0.560.74)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 1 / 19.9Missense obs/exp: 138 / 214.6Syn Z: 0.59

ClinVar Variant Classifications

177 submitted variants in ClinVar

Classification Summary

Pathogenic93
Likely Pathogenic11
VUS55
Likely Benign1
Benign1
93
Pathogenic
11
Likely Pathogenic
55
VUS
1
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
93
0
93
Likely Pathogenic
0
0
11
0
11
VUS
0
40
15
0
55
Likely Benign
0
1
0
0
1
Benign
0
0
0
1
1
Total0411191161

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

PPP1R7 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC