PPP1R2C

Chr X

PPP1R2 family member C

Also known as: I-4, PPP1R2P9

The protein functions as a protein phosphatase inhibitor, specifically inhibiting the catalytic subunit of PP1 and weakly inhibiting myosin-associated phosphatases in intracellular signal transduction. Mutations in this gene have been associated with neurodevelopmental disorders, though the specific phenotypic spectrum and inheritance pattern require further clinical characterization. Additional clinical and genetic data are needed to fully define the disease associations for this gene.

OMIMResearchSummary from RefSeq, UniProt
DNmechanism

Population Genetics & Constraint

Constraint data not available from gnomAD.

DN
0.6938th %ile
GOF
0.4972th %ile
LOF
0.2679th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PPP1R2C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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