PPM1L

Chr 3

protein phosphatase, Mg2+/Mn2+ dependent 1L

Also known as: PP2C-epsilon, PP2CE, PPM1-LIKE

The protein encoded by this gene is a magnesium or manganese-requiring phosphatase that is involved in several signaling pathways. The encoded protein downregulates apoptosis signal-regulating kinase 1, a protein that initiates a signaling cascade that leads to apoptosis when cells are subjected to cytotoxic stresses. This protein also is an endoplasmic reticulum transmembrane protein that helps regulate ceramide transport from the endoplasmic reticulum to the Golgi apparatus. Finally, this gene may be involved in adiposity since it is upregulated in adipose tissues. Several transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Dec 2015]

OMIMResearchGenerating clinical summary…
LOEUF 0.54
Clinical SummaryPPM1L
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.21) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.54LOEUF
pLI 0.473
Z-score 2.80
OE 0.21 (0.090.54)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
2.06Z-score
OE missense 0.60 (0.510.69)
123 obs / 206.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.21 (0.090.54)
00.351.4
Missense OE?0.60 (0.510.69)
00.61.4
Synonymous OE?1.03
01.21.6
LoF obs/exp: 3 / 14.5Missense obs/exp: 123 / 206.4Syn Z: -0.19

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PPM1L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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