POP1

Chr 8AR

POP1 homolog, ribonuclease P/MRP subunit

The protein functions as a ribonuclease that processes pre-RNA in both the endoribonuclease for mitochondrial RNA processing complex and the ribonuclease P complex. Mutations cause anauxetic dysplasia 2, a skeletal dysplasia syndrome, with autosomal recessive inheritance. This gene shows low constraint against loss-of-function variants (pLI near 0), suggesting tolerance to such changes in the general population.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.761 OMIM phenotype
Clinical SummaryPOP1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.76LOEUF
pLI 0.000
Z-score 2.97
OE 0.56 (0.410.76)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.12Z-score
OE missense 0.87 (0.810.94)
495 obs / 570.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.56 (0.410.76)
00.351.4
Missense OE0.87 (0.810.94)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 29 / 52.2Missense obs/exp: 495 / 570.3Syn Z: 1.28

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

POP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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