POLR1C

Chr 6AR

RNA polymerase I and III subunit C

Also known as: AC40, HLD11, RPA39, RPA40, RPA5, RPAC1, RPC40, TCS3

The protein encoded by this gene is a subunit of both RNA polymerase I and RNA polymerase III complexes. The encoded protein is part of the Pol core element. Mutations in this gene have been associated with Treacher Collins syndrome (TCS) and hypomyelinating leukodystrophy 11. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016]

OMIMResearchGenerating clinical summary…
LOFmechanismARLOEUF 1.402 OMIM phenotypes
Clinical SummaryPOLR1C
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Gene-Disease Validity (ClinGen)
Treacher Collins syndrome 3 · ARModerate

Moderate evidence — consider for supplementary testing

2 total gene-disease associations curated

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.40LOEUF
pLI 0.000
Z-score 0.34
OE 0.91 (0.611.40)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.44Z-score
OE missense 1.29 (1.161.43)
252 obs / 195.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.91 (0.611.40)
00.351.4
Missense OE?1.29 (1.161.43)
00.61.4
Synonymous OE?1.24
01.21.6
LoF obs/exp: 15 / 16.5Missense obs/exp: 252 / 195.2Syn Z: -1.58

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

POLR1C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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