PLEKHG6

Chr 12

pleckstrin homology and RhoGEF domain containing G6

Also known as: ARHGEF46, MyoGEF

Predicted to enable guanyl-nucleotide exchange factor activity. Predicted to be involved in regulation of small GTPase mediated signal transduction. Located in cell junction and centrosome. [provided by Alliance of Genome Resources, Jul 2025]

0
Active trials
2
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.00
LOEUF
GOF
Mechanism· predicted
Clinical SummaryPLEKHG6
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.00LOEUF
pLI 0.000
Z-score 1.55
OE 0.75 (0.571.00)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.00Z-score
OE missense 1.00 (0.931.08)
462 obs / 462.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.75 (0.571.00)
00.351.4
Missense OE1.00 (0.931.08)
00.61.4
Synonymous OE1.06
01.21.6
LoF obs/exp: 35 / 46.4Missense obs/exp: 462 / 462.0Syn Z: -0.68
DN
0.6065th %ile
GOF
0.71top 25%
LOF
0.3941th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PLEKHG6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗