PLD1

Chr 3AR

phospholipase D1

Also known as: CVDD, CVDP1

This gene encodes a phosphatidylcholine-specific phospholipase which catalyzes the hydrolysis of phosphatidylcholine in order to yield phosphatidic acid and choline. The enzyme may play a role in signal transduction and subcellular trafficking. Alternative splicing results in multiple transcript variants with both catalytic and regulatory properties. [provided by RefSeq, Sep 2011]

OMIMResearchGenerating clinical summary…
LOFmechanismARLOEUF 0.881 OMIM phenotype
Clinical SummaryPLD1
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Gene-Disease Validity (ClinGen)
PLD1-related congenital heart disease · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.88LOEUF
pLI 0.000
Z-score 2.36
OE 0.68 (0.530.88)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.18Z-score
OE missense 0.98 (0.921.05)
602 obs / 614.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.68 (0.530.88)
00.351.4
Missense OE?0.98 (0.921.05)
00.61.4
Synonymous OE?0.92
01.21.6
LoF obs/exp: 42 / 62.0Missense obs/exp: 602 / 614.8Syn Z: 0.96
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitivePLD1-related cardiac valvular dysplasiaLOFAR

This gene — mechanism propensity

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.6842th %ile
GOF
0.7027th %ile
LOF
0.3066th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PLD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.