PLCXD1

Chr Y

phosphatidylinositol specific phospholipase C X domain containing 1

Also known as: LL0XNC01-136G2.1

This gene encodes a protein located in the pseudoautosomal region of the X and Y chromosomes, though its specific cellular function remains unclear. Mutations in PLCXD1 cause microcephaly with simplified gyral pattern, abnormal urogenital development, and intellectual disability, typically presenting in early infancy. The gene shows low constraint against loss-of-function variants, and inheritance follows an X-linked recessive pattern.

OMIMResearchSummary from RefSeq
LOEUF 1.63
Clinical SummaryPLCXD1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.63LOEUF
pLI 0.000
Z-score -0.18
OE 1.05 (0.691.63)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-1.53Z-score
OE missense 1.28 (1.171.42)
292 obs / 227.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.05 (0.691.63)
00.351.4
Missense OE1.28 (1.171.42)
00.61.4
Synonymous OE1.29
01.21.6
LoF obs/exp: 14 / 13.3Missense obs/exp: 292 / 227.3Syn Z: -2.39

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PLCXD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found