PLCH1

Chr 3AR

phospholipase C eta 1

Also known as: HPE14, PLC eta 1, PLC-L3, PLCL3

PLCH1 is a member of the PLC-eta family of the phosphoinositide-specific phospholipase C (PLC) superfamily of enzymes that cleave phosphatidylinositol 4,5-bisphosphate (PtdIns(4,5)P2) to generate second messengers inositol 1,4,5-trisphosphate (IP3) and diacylglycerol (DAG) (Hwang et al., 2005 [PubMed 15702972]).[supplied by OMIM, Jun 2009]

OMIMResearchGenerating clinical summary…
ARLOEUF 0.341 OMIM phenotype
Clinical SummaryPLCH1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.23) despite low pLI — interpret in context.
📋
ClinVar Variants
93 VUS of 98 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint?
0.34LOEUF
pLI 0.396
Z-score 6.23
OE 0.23 (0.150.34)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint?
1.48Z-score
OE missense 0.86 (0.810.91)
777 obs / 901.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.23 (0.150.34)
00.351.4
Missense OE?0.86 (0.810.91)
00.61.4
Synonymous OE?0.93
01.21.6
LoF obs/exp: 17 / 75.4Missense obs/exp: 777 / 901.9Syn Z: 1.07

ClinVar Variant Classifications

98 submitted variants in ClinVar

Classification Summary

VUS93
Likely Benign4
Conflicting1
93
VUS
4
Likely Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
0
0
0
Likely Pathogenic
0
0
0
0
0
VUS
0
93
0
0
93
Likely Benign
0
1
0
3
4
Benign
0
0
0
0
0
Conflicting
1
Total0940398

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

1 pathogenic / likely-pathogenic (of 2) ClinVar copy-number / structural variants overlap PLCH1 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

PLCH1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →