PINK1

Chr 1

PTEN induced kinase 1

Also known as: BRPK, PARK6

This gene encodes a serine/threonine protein kinase that localizes to mitochondria. It is thought to protect cells from stress-induced mitochondrial dysfunction. Mutations in this gene cause one form of autosomal recessive early-onset Parkinson disease. [provided by RefSeq, Jul 2008]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtParkinson disease 6

Clinical highlights

Gene-disease validity (ClinGen)
Parkinson disease · ARDefinitivesufficient evidence for diagnostic panels
3
Active trials
1686
Pubs (1 yr)
P/LP submissions
P/LP missense
1.14
LOEUF
Mechanism
📖
GeneReview available — PINK1
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.14LOEUF
pLI 0.000
Z-score 1.05
OE 0.77 (0.531.14)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.13Z-score
OE missense 0.98 (0.891.08)
308 obs / 314.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.77 (0.531.14)
00.351.4
Missense OE?0.98 (0.891.08)
00.61.4
Synonymous OE?1.19
01.21.6
LoF obs/exp: 18 / 23.5Missense obs/exp: 308 / 314.4Syn Z: -1.76

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PINK1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.