PIGM

Chr 1AR

phosphatidylinositol glycan anchor biosynthesis class M

Also known as: GPI-MT-I

This gene encodes a transmembrane protein that is located in the endoplasmic reticulum and is involved in GPI-anchor biosynthesis. The glycosylphosphatidylinositol (GPI)-anchor is a glycolipid which contains three mannose molecules in its core backbone. The GPI-anchor is found on many blood cells and serves to anchor proteins to the cell surface. This gene encodes a mannosyltransferase, GPI-MT-I, that transfers the first mannose to GPI on the lumenal side of the endoplasmic reticulum. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Glycosylphosphatidylinositol deficiencyMIM #610293
AR

Clinical highlights

Gene-disease validity (ClinGen)
congenital disorder of glycosylation · ARLimitednot for standalone diagnostic reporting
0
Active trials
11
Pubs (1 yr)
P/LP submissions
P/LP missense
1.25
LOEUF
DN
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.25LOEUF
pLI 0.000
Z-score 0.96
OE 0.70 (0.411.25)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.08Z-score
OE missense 1.02 (0.911.14)
215 obs / 211.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.70 (0.411.25)
00.351.4
Missense OE?1.02 (0.911.14)
00.61.4
Synonymous OE?0.99
01.21.6
LoF obs/exp: 8 / 11.5Missense obs/exp: 215 / 211.7Syn Z: 0.09

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PIGM · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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