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PIERS

Chr 3AR

laminin subunit beta 2

Also known as: LAMS, NPHS5, PIERS

The LAMB2 gene encodes the laminin beta-2 chain, a glycoprotein component of basement membranes that is particularly enriched at neuromuscular junctions and in kidney glomeruli. Mutations cause Pierson syndrome, an autosomal recessive disorder characterized by congenital nephrotic syndrome and ocular abnormalities including microcoria. This condition typically presents in the neonatal period with severe renal dysfunction and distinctive eye findings.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Clinical SummaryPIERS
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/PIERS?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PIERS · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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