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PHRINL

Chr 1AR

ATPase family AAA domain containing 3A

Also known as: HAYOS, PHRINL

The protein is a mitochondrial membrane protein that regulates mitochondrial dynamics, nucleoid organization, protein translation, cell growth, and cholesterol metabolism. Mutations cause pontocerebellar hypoplasia, hypotonia, and respiratory insufficiency syndrome, a neonatal lethal condition also known as Harel-Yoon syndrome. The disorder follows autosomal recessive inheritance with severe neonatal onset affecting the brain, muscle tone, and respiratory system.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/PHRINL?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PHRINL · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

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