PHF13

Chr 1

PHD finger protein 13

Also known as: PHF5, SPOC1

PHF13 encodes a chromatin-binding protein that regulates chromosome condensation during mitosis and modulates DNA damage response by recruiting corepressors and histone methyltransferases. The gene is highly constrained against loss-of-function variants (pLI 0.98, LOEUF 0.25), but specific disease associations and inheritance patterns have not yet been established in humans. Based on functional studies, mutations would likely affect cell division and chromatin regulation processes.

Summary from RefSeq, UniProt
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0
Active trials
2
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.25
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryPHF13
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.98). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.25LOEUF
pLI 0.980
Z-score 3.21
OE 0.00 (0.000.25)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.76Z-score
OE missense 0.64 (0.560.75)
124 obs / 192.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.25)
00.351.4
Missense OE0.64 (0.560.75)
00.61.4
Synonymous OE1.26
01.21.6
LoF obs/exp: 0 / 12.0Missense obs/exp: 124 / 192.8Syn Z: -1.88
DN
0.3196th %ile
GOF
0.2298th %ile
LOF
0.83top 5%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.25

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PHF13 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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