PHF11

Chr 13

PHD finger protein 11

Also known as: APY, BCAP, IGEL, IGER, IGHER, NY-REN-34, NYREN34

This gene encodes a protein containing a PHD-type zinc finger that acts as a positive regulator of Th1-type cytokine gene expression. The gene has been identified as a candidate gene for asthma in some studies. PHF11 shows low constraint against loss-of-function variants (LOEUF 1.278), suggesting tolerance to such mutations.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
2
Pubs (1 yr)
61
P/LP submissions
0%
P/LP missense
1.28
LOEUF
DN
Mechanism· predicted
Clinical SummaryPHF11
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
61 unique Pathogenic / Likely Pathogenic· 49 VUS of 130 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.28LOEUF
pLI 0.000
Z-score 0.73
OE 0.80 (0.521.28)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.04Z-score
OE missense 0.77 (0.660.89)
121 obs / 157.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.80 (0.521.28)
00.351.4
Missense OE0.77 (0.660.89)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 13 / 16.2Missense obs/exp: 121 / 157.6Syn Z: 0.68
DN
0.6259th %ile
GOF
0.5170th %ile
LOF
0.3649th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

130 submitted variants in ClinVar

Classification Summary

Pathogenic59
Likely Pathogenic2
VUS49
Likely Benign5
Benign3
59
Pathogenic
2
Likely Pathogenic
49
VUS
5
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
59
0
59
Likely Pathogenic
0
0
2
0
2
VUS
0
41
8
0
49
Likely Benign
1
2
1
1
5
Benign
0
0
2
1
3
Total143722118

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

PHF11 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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