PEDS1-UBE2V1

Chr 20

PEDS1-UBE2V1 readthrough

Also known as: CROC-1B, CROC1B, KUA-UEV, TMEM189-UBE2V1

The protein encoded by this read-through transcript contains UEV1 B domains and localizes to the cytoplasm, but its biological function remains undetermined. This gene shows low constraint against loss-of-function variants (pLI = 0.008, LOEUF = 0.67), and no established disease associations have been reported in the literature.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
10
P/LP submissions
0%
P/LP missense
0.67
LOEUF
Mechanism
Clinical SummaryPEDS1-UBE2V1
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
10 unique Pathogenic / Likely Pathogenic· 9 VUS of 23 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.67LOEUF
pLI 0.008
Z-score 2.65
OE 0.36 (0.200.67)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
2.43Z-score
OE missense 0.53 (0.450.62)
112 obs / 211.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.36 (0.200.67)
00.351.4
Missense OE0.53 (0.450.62)
00.61.4
Synonymous OE1.17
01.21.6
LoF obs/exp: 7 / 19.7Missense obs/exp: 112 / 211.4Syn Z: -1.18

ClinVar Variant Classifications

23 submitted variants in ClinVar

Classification Summary

Pathogenic7
Likely Pathogenic3
VUS9
Likely Benign1
Benign1
7
Pathogenic
3
Likely Pathogenic
9
VUS
1
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
7
0
7
Likely Pathogenic
0
0
3
0
3
VUS
1
6
2
0
9
Likely Benign
0
1
0
0
1
Benign
0
0
0
1
1
Total1712121

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

PEDS1-UBE2V1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found