PDGFRL

Chr 8

platelet derived growth factor receptor like

Also known as: PDGRL, PRLTS

The protein shares significant sequence similarity with the ligand binding domain of platelet-derived growth factor receptor beta and functions as a tumor suppressor. Mutations cause somatic colorectal cancer and hepatocellular cancer, indicating these are acquired rather than inherited cancers. This gene is highly intolerant to loss-of-function variants in the general population, consistent with its tumor suppressor role.

Summary from RefSeq, OMIM
Research Assistant →

Primary Disease Associations & Inheritance

Colorectal cancer, somaticMIM #114500
Hepatocellular cancer, somaticMIM #114550
0
Active trials
5
Pubs (1 yr)
82
P/LP submissions
1%
P/LP missense
1.79
LOEUF
Mechanism
Clinical SummaryPDGFRL
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
82 unique Pathogenic / Likely Pathogenic· 90 VUS of 196 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.79LOEUF
pLI 0.000
Z-score -0.96
OE 1.27 (0.881.79)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-2.00Z-score
OE missense 1.38 (1.261.52)
303 obs / 219.6 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.27 (0.881.79)
00.351.4
Missense OE1.38 (1.261.52)
00.61.4
Synonymous OE1.35
01.21.6
LoF obs/exp: 19 / 15.0Missense obs/exp: 303 / 219.6Syn Z: -2.62

ClinVar Variant Classifications

196 submitted variants in ClinVar

Classification Summary

Pathogenic78
Likely Pathogenic4
VUS90
Likely Benign4
Benign2
Conflicting2
78
Pathogenic
4
Likely Pathogenic
90
VUS
4
Likely Benign
2
Benign
2
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
1
77
0
78
Likely Pathogenic
0
0
4
0
4
VUS
0
81
9
0
90
Likely Benign
0
2
1
1
4
Benign
0
1
0
1
2
Conflicting
2
Total085912180

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

PDGFRL · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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