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PCH3

Chr 7AR

piccolo presynaptic cytomatrix protein

Also known as: ACZ, PCH3

The protein encoded by this gene is part of the presynaptic cytoskeletal matrix that establishes active synaptic zones and regulates synaptic vesicle trafficking. Mutations cause pontocerebellar hypoplasia type 3, a severe neurodevelopmental disorder affecting the brainstem and cerebellum. Inheritance is autosomal recessive.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/PCH3?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

PCH3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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