OR8D2

Chr 11

olfactory receptor family 8 subfamily D member 2

Also known as: JCG2

OR8D2 encodes an olfactory receptor that interacts with odorant molecules to initiate neuronal responses triggering smell perception and may be involved in taste perception. This gene is a segregating pseudogene where some individuals carry functional alleles while others have non-functional variants, but no specific diseases have been established from OR8D2 mutations. The gene shows low constraint to loss-of-function variation (pLI = 0.21, LOEUF = 1.49), consistent with tolerance to functional loss.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
57
P/LP submissions
0%
P/LP missense
1.49
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryOR8D2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.34) despite low pLI — interpret in context.
📋
ClinVar Variants
57 unique Pathogenic / Likely Pathogenic· 60 VUS of 119 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.49LOEUF
pLI 0.211
Z-score 1.04
OE 0.34 (0.121.49)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.26Z-score
OE missense 0.94 (0.831.08)
154 obs / 163.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.34 (0.121.49)
00.351.4
Missense OE0.94 (0.831.08)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 1 / 2.9Missense obs/exp: 154 / 163.4Syn Z: 0.67
DN
0.85top 5%
GOF
0.86top 5%
LOF
0.1598th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

119 submitted variants in ClinVar

Classification Summary

Pathogenic55
Likely Pathogenic2
VUS60
Likely Benign2
55
Pathogenic
2
Likely Pathogenic
60
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
55
0
55
Likely Pathogenic
0
0
2
0
2
VUS
0
57
3
0
60
Likely Benign
0
1
0
1
2
Benign
0
0
0
0
0
Total058601119

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

OR8D2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found