OR2L13

Chr 1

olfactory receptor family 2 subfamily L member 13

OR2L13 encodes an olfactory receptor that detects odorant molecules in the nose and initiates G protein-coupled signaling to trigger smell perception. This gene shows very low constraint against loss-of-function variants (pLI = 0.001, LOEUF = 1.58), and no Mendelian diseases have been associated with OR2L13 mutations in current databases. Olfactory receptor genes like OR2L13 are generally considered to have little clinical significance in pediatric neurology practice.

ResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 1.58
Clinical SummaryOR2L13
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.58LOEUF
pLI 0.001
Z-score 0.52
OE 0.78 (0.401.58)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.24Z-score
OE missense 1.05 (0.931.19)
180 obs / 171.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.78 (0.401.58)
00.351.4
Missense OE1.05 (0.931.19)
00.61.4
Synonymous OE1.25
01.21.6
LoF obs/exp: 5 / 6.4Missense obs/exp: 180 / 171.3Syn Z: -1.58
DN
0.86top 5%
GOF
0.82top 10%
LOF
0.1697th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

OR2L13 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found