OR2K2

Chr 9

olfactory receptor family 2 subfamily K member 2

Also known as: HSHTPCRH06, HTPCRH06, OR2AN1P, OR2AR1P

The OR2K2 protein is an odorant receptor that binds odor molecules in the nose and initiates G-protein-coupled signaling to trigger smell perception through its 7-transmembrane domain structure. No pediatric neurogenetic diseases have been definitively associated with OR2K2 mutations based on the available data. The predicted gain-of-function mechanism and low constraint scores suggest this gene may tolerate functional variants without causing disease.

ResearchSummary from RefSeq, UniProt, Mechanism
MultiplemechanismLOEUF 1.54
Clinical SummaryOR2K2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.54LOEUF
pLI 0.001
Z-score 0.59
OE 0.75 (0.391.54)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.03Z-score
OE missense 1.01 (0.891.14)
175 obs / 174.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.75 (0.391.54)
00.351.4
Missense OE1.01 (0.891.14)
00.61.4
Synonymous OE1.16
01.21.6
LoF obs/exp: 5 / 6.6Missense obs/exp: 175 / 174.0Syn Z: -1.10
DN
0.85top 5%
GOF
0.86top 5%
LOF
0.1399th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

OR2K2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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