OR2G3

Chr 1

olfactory receptor family 2 subfamily G member 3

Also known as: OR1-33

OR2G3 encodes an olfactory receptor that functions as a G-protein-coupled receptor to detect odorant molecules and initiate smell perception through neuronal signaling. This gene is not known to be associated with any Mendelian diseases or clinical phenotypes in humans. The gene shows low constraint against loss-of-function variants (LOEUF 1.42), consistent with the general tolerance of olfactory receptor genes to variation.

ResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 1.42
Clinical SummaryOR2G3
Population Constraint (gnomAD)
Low constraint (pLI 0.08) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
70 unique Pathogenic / Likely Pathogenic· 70 VUS of 147 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.42LOEUF
pLI 0.079
Z-score 1.02
OE 0.47 (0.191.42)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.05Z-score
OE missense 0.99 (0.871.13)
158 obs / 159.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.47 (0.191.42)
00.351.4
Missense OE0.99 (0.871.13)
00.61.4
Synonymous OE0.97
01.21.6
LoF obs/exp: 2 / 4.3Missense obs/exp: 158 / 159.8Syn Z: 0.16
DN
0.85top 5%
GOF
0.83top 10%
LOF
0.1598th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

147 submitted variants in ClinVar

Classification Summary

Pathogenic64
Likely Pathogenic6
VUS70
Likely Benign4
Benign3
64
Pathogenic
6
Likely Pathogenic
70
VUS
4
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
64
0
64
Likely Pathogenic
0
0
6
0
6
VUS
0
48
22
0
70
Likely Benign
0
3
1
0
4
Benign
0
2
1
0
3
Total053940147

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

OR2G3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found