OR1L1

Chr 9

olfactory receptor family 1 subfamily L member 1

The OR1L1 protein is an olfactory receptor that recognizes and transduces odorant signals through G protein-coupled receptor mechanisms in the nose to initiate smell perception. Based on the provided information, there are no established disease associations or inheritance patterns documented for OR1L1 mutations.

Summary from RefSeq, UniProt, Mechanism
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0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.84
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryOR1L1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.00) despite low pLI — interpret in context.
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.84LOEUF
pLI 0.333
Z-score 0.64
OE 0.00 (0.001.84)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.09Z-score
OE missense 1.02 (0.901.16)
163 obs / 159.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.00 (0.001.84)
00.351.4
Missense OE1.02 (0.901.16)
00.61.4
Synonymous OE0.82
01.21.6
LoF obs/exp: 0 / 0.5Missense obs/exp: 163 / 159.8Syn Z: 1.10
DN
0.86top 5%
GOF
0.81top 10%
LOF
0.1994th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

OR1L1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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