OR1B1

Chr 9

olfactory receptor family 1 subfamily B member 1

The protein functions as an odorant receptor involved in smell detection. Mutations in this gene cause autosomal recessive congenital anosmia, resulting in complete absence of the sense of smell from birth. The gene shows low constraint against loss-of-function variants, consistent with its role in a non-essential sensory function.

ResearchSummary from UniProt
MultiplemechanismLOEUF 1.80
Clinical SummaryOR1B1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.80LOEUF
pLI 0.000
Z-score -0.17
OE 1.07 (0.601.80)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.04Z-score
OE missense 0.99 (0.881.12)
184 obs / 185.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.07 (0.601.80)
00.351.4
Missense OE0.99 (0.881.12)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 7 / 6.5Missense obs/exp: 184 / 185.7Syn Z: -0.13
DN
0.86top 5%
GOF
0.86top 5%
LOF
0.1499th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

OR1B1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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