OR13F1

Chr 9

olfactory receptor family 13 subfamily F member 1

Also known as: OR9-6

OR13F1 encodes an olfactory receptor that binds odorant molecules and initiates G-protein-coupled signaling to trigger smell perception. No pediatric neurological diseases have been definitively associated with OR13F1 mutations in the provided data. The low pLI score and high LOEUF score suggest this gene is tolerant to loss-of-function variants, with a predicted gain-of-function mechanism for any potential pathogenic variants.

Summary from RefSeq, UniProt, Mechanism
Research Assistant →
0
Active trials
0
Pubs (1 yr)
36
P/LP submissions
0%
P/LP missense
1.83
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryOR13F1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
36 unique Pathogenic / Likely Pathogenic· 52 VUS of 93 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.83LOEUF
pLI 0.000
Z-score -0.28
OE 1.12 (0.631.83)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.36Z-score
OE missense 1.08 (0.961.22)
183 obs / 169.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.12 (0.631.83)
00.351.4
Missense OE1.08 (0.961.22)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 7 / 6.2Missense obs/exp: 183 / 169.7Syn Z: -0.49
DN
0.7132th %ile
GOF
0.7126th %ile
LOF
0.2774th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

93 submitted variants in ClinVar

Classification Summary

Pathogenic34
Likely Pathogenic2
VUS52
Likely Benign5
34
Pathogenic
2
Likely Pathogenic
52
VUS
5
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
34
0
34
Likely Pathogenic
0
0
2
0
2
VUS
0
45
7
0
52
Likely Benign
0
4
1
0
5
Benign
0
0
0
0
0
Total04944093

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

OR13F1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found