OPN1MW2

Chr X

opsin 1, medium wave sensitive 2

Also known as: GOP

The encoded protein is a G-protein coupled receptor that functions as green cone photopigment (medium-wavelength sensitive opsin) for color vision by absorbing light and mediating visual signal transduction. Mutations cause deutanopic colorblindness through an X-linked recessive inheritance pattern. The pathogenic mechanism involves gain-of-function effects, often resulting from unequal recombination events between the tandemly arrayed opsin genes on the X chromosome.

Summary from RefSeq, UniProt, Mechanism
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0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.36
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryOPN1MW2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.30) despite low pLI — interpret in context.
Some data sources returned errors (1)

ensembl: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.36LOEUF
pLI 0.245
Z-score 1.19
OE 0.30 (0.101.36)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.35Z-score
OE missense 0.87 (0.691.10)
51 obs / 58.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.30 (0.101.36)
00.351.4
Missense OE0.87 (0.691.10)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 1 / 3.3Missense obs/exp: 51 / 58.6Syn Z: 0.03
DN
0.74top 25%
GOF
0.76top 25%
LOF
0.3260th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

OPN1MW2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found