OLFM1

Chr 9

olfactomedin 1

Also known as: AMY, NOE1, NOELIN1, OlfA

The protein inhibits interactions between RTN4R and LINGO1 to regulate axonal growth in the embryonic and adult central nervous system and may contribute to neural crest cell production and olfactory responses. Mutations cause autosomal recessive intellectual disability with seizures and hypotonia. This gene is highly constrained against loss-of-function variants (pLI = 1.0, LOEUF = 0.22), indicating intolerance to protein-truncating mutations.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.22
Clinical SummaryOLFM1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint
0.22LOEUF
pLI 0.997
Z-score 4.08
OE 0.05 (0.020.22)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
3.41Z-score
OE missense 0.44 (0.380.51)
131 obs / 296.1 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios
LoF OE0.05 (0.020.22)
00.351.4
Missense OE0.44 (0.380.51)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 1 / 21.3Missense obs/exp: 131 / 296.1Syn Z: 0.58
DN
0.4883th %ile
GOF
0.4085th %ile
LOF
0.65top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.22

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

OLFM1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →