NUP214

Chr 9

nucleoporin 214

Also known as: CAIN, CAN, IIAE9

The protein is a nucleoporin that forms part of the nuclear pore complex and is essential for nucleocytoplasmic transport and proper cell cycle progression. Mutations cause autosomal recessive acute infection-induced encephalopathy with increased susceptibility during febrile episodes. The gene is highly constrained against loss-of-function variation (LOEUF 0.35), indicating that biallelic mutations likely have severe consequences for cellular function.

ResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismLOEUF 0.35
Clinical SummaryNUP214
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.24) despite low pLI — interpret in context.
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Clinical Trials
2 active or recruiting trials — potential therapeutic options may be available
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.35LOEUF
pLI 0.055
Z-score 6.53
OE 0.24 (0.170.35)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
0.65Z-score
OE missense 0.95 (0.900.99)
1063 obs / 1124.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.24 (0.170.35)
00.351.4
Missense OE0.95 (0.900.99)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 21 / 86.5Missense obs/exp: 1063 / 1124.7Syn Z: -0.31

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NUP214 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
SET-NUP214
Zheng YZ et al.·Zhonghua Xue Ye Xue Za Zhi
2021
SET-NUP214 24
Chen SM et al.·Zhonghua Xue Ye Xue Za Zhi
2021
DEK-NUP214 1
Li XZ et al.·Zhonghua Xue Ye Xue Za Zhi
2024
DEK-NUP214 12
Shen YY et al.·Zhonghua Xue Ye Xue Za Zhi
2024
Top 5 full-text resultsSearch PubTator3 ↗