The NUDT7 protein functions as a fatty acyl-coenzyme A diphosphatase that hydrolyzes fatty acyl-CoA substrates and may regulate CoA levels in peroxisomes in response to metabolic demand. The gene shows very low intolerance to loss-of-function mutations (pLI near 0) and high tolerance to missense variants (LOEUF 1.915), but no specific disease associations with NUDT7 mutations have been established. Based on the available data, the clinical significance of NUDT7 variants in pediatric neurogenetics remains unclear.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
6
Pubs (1 yr)
28
P/LP submissions
0%
P/LP missense
1.92
LOEUF
Mechanism
Clinical SummaryNUDT7
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
28 unique Pathogenic / Likely Pathogenic· 81 VUS of 125 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.92LOEUF
pLI 0.000
Z-score -0.88
OE 1.40 (0.781.92)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.83Z-score
OE missense 1.20 (1.051.36)
164 obs / 136.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.40 (0.781.92)
00.351.4
Missense OE1.20 (1.051.36)
00.61.4
Synonymous OE1.32
01.21.6
LoF obs/exp: 8 / 5.7Missense obs/exp: 164 / 136.8Syn Z: -1.82

ClinVar Variant Classifications

125 submitted variants in ClinVar

Classification Summary

Pathogenic26
Likely Pathogenic2
VUS81
Likely Benign5
Benign1
26
Pathogenic
2
Likely Pathogenic
81
VUS
5
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
26
0
26
Likely Pathogenic
0
0
2
0
2
VUS
0
51
30
0
81
Likely Benign
0
3
2
0
5
Benign
0
0
1
0
1
Total054610115

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

NUDT7 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗